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Arrhythmogenic Right Ventricular Cardiomyopathy: Difference between revisions
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Arrhythmogenic Right Ventricular Cardiomyopathy (view source)
Revision as of 03:37, 11 May 2009
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[[Image:epsilon_wave.png|thumb|ECG with an epsilon wave in V1]] | [[Image:epsilon_wave.png|thumb|ECG with an epsilon wave in V1]] | ||
[[Image:arvdhart.png|thumb| A section throught the heart of a ARVC patient. (A) Transmural fatty replacement of the right ventricular free wall. (B) Myocardial atrophy is confined to the right ventricle and substantially spares the interventricular septum as well as the left ventricular free wall. <cite>Corrado</cite> Reproduced with permission from BMJ Publishing Group Ltd. ]] | [[Image:arvdhart.png|thumb| A section throught the heart of a ARVC patient. (A) Transmural fatty replacement of the right ventricular free wall. (B) Myocardial atrophy is confined to the right ventricle and substantially spares the interventricular septum as well as the left ventricular free wall. <cite>Corrado</cite> Reproduced with permission from BMJ Publishing Group Ltd. ]] | ||
'''Arrythmogenic Right Ventricular Cardiomyopathy''', (ARVC, or ARVD: Arrythmogenic Right Ventricular Disease) is characterized by fatty replacement and fibrosis of the heart. Especially the right ventricle apex and outflow tract are involved. However the left ventricle can be affected to.<cite>Corr</cite> | |||
'''Arrythmogenic Right Ventricular Cardiomyopathy''', (ARVC, or ARVD: Arrythmogenic Right Ventricular Disease) is characterized by fatty replacement and fibrosis of the heart. Especially the right ventricle apex and outflow tract are involved. However the left ventricle can be affected to. | |||
As a result of the fatty replacement and fibrosis, ventricular arrhythmias are common in this disease and can lead to palpitations, syncope and sudden death. At older age right ventricular pump failure can occur. | As a result of the fatty replacement and fibrosis, ventricular arrhythmias are common in this disease and can lead to palpitations, syncope and sudden death. At older age right ventricular pump failure can occur. | ||
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'''Treatment''' focuses on avoiding complications.<cite>ACC2006</cite> | '''Treatment''' focuses on avoiding complications.<cite>ACC2006</cite> | ||
*Medication: | *Medication: | ||
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*[[ICD]]] implantation can be considered for the prevention of sudden cardiac death in patients with ARVC with extensive disease, including those with left ventricular involvement, 1 or more affected family member with SCD, or undiagnosed syncope when [[Ventricular Tachycardia|ventricular tachycardia]] or [[Ventricular Fibrillation|ventricular Fibrillation]] has not been excluded as the cause of syncope, who are receiving chronic optimal medical therapy, and who have reasonable expectation of survival with a good functional status for more than 1 y. | *[[ICD]]] implantation can be considered for the prevention of sudden cardiac death in patients with ARVC with extensive disease, including those with left ventricular involvement, 1 or more affected family member with SCD, or undiagnosed syncope when [[Ventricular Tachycardia|ventricular tachycardia]] or [[Ventricular Fibrillation|ventricular Fibrillation]] has not been excluded as the cause of syncope, who are receiving chronic optimal medical therapy, and who have reasonable expectation of survival with a good functional status for more than 1 y. | ||
*Radiofrequency [[ablation]] can be useful as adjunctive therapy in management of patients with ARVC with recurrent [[Ventricular Tachycardia|ventricular tachycardia]], despite optimal antiarrhythmic drug therapy. | *Radiofrequency [[ablation]] can be useful as adjunctive therapy in management of patients with ARVC with recurrent [[Ventricular Tachycardia|ventricular tachycardia]], despite optimal antiarrhythmic drug therapy. | ||
<gallery> | |||
Image:arvd_ecg1.png | |||
Image:arvd_ecg2.png | |||
Image:arvd_ecg3.png | |||
</gallery> | |||
==Referenties== | ==Referenties== | ||
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#Corrado pmid=10768917 | #Corrado pmid=10768917 | ||
#ACC2006 pmid=16949478 | #ACC2006 pmid=16949478 | ||
#Corr pmid=19366719 | |||
</biblio> | </biblio> | ||