ECG in Congenital Heart Disease: Difference between revisions

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Congenital Heart Disease can result in ECG changes, often related to atrial or ventricular overload and  enlargement. Below a list of relatively common forms of congenital heart disease and their potential ECG changes. Adapted from Khairy et al.<cite>khairy</cite>
==Secundum atrial septal defect==
==Secundum atrial septal defect==
Information about [[w:Atrial_septal_defect|Secundum atrial septal defec on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, increased risk of AF with age
*[[Rhythm]]: normal sinus rhythm, increased risk of AF with age
*[[Conduction|PR interval]]: first degree AV block in 6-19%
*[[Conduction|PR interval]]: first degree AV block in 6-19%
*[[Heart axis|QRS axis]]: 0° to 180°; RAD; LAHB
*[[Heart axis|QRS axis]]: 0° to 180°; RAD; LAD in Holt-Oram or LAHB
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]:
* QRS Configuration: rSr&acute; or rsR&acute; with RBBBi&gt;RBBBc
*Particularities: “Crochetage” pattern
* Atrial Enlargement: RAE 35%
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Uncommon
*Particularities: "Crochetage" pattern
 
==Ventricular Septal Defect==
==Ventricular Septal Defect==
Information about [[w:Ventricular_septal_defect|Ventricular Septal Defect on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, PVCs
*[[Conduction|PR interval]]: Normal or mild &uarr;; 1° AVB 10%
*[[Heart axis|QRS axis]]: RAD with BVH; LAD 3% to 15%
* QRS Configuration: Normal or rsr&acute;; possible RBBB
* Atrial Enlargement: Possible RAE&plusmn;LAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: BVH 23% to 61%; RVH with Eisenmenger
*Particularities: Katz-Wachtel phenomenon
==AV canal defect==
Information about [[w:Atrioventricular_septal_defect|AV canal defect on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, PVCs 30%
*[[Conduction|PR interval]]: 1° AVB &gt;50%
*[[Heart axis|QRS axis]]: Moderate to extreme LAD; normal with atypical
* QRS Configuration: rSr&acute; or rsR&acute;
* Atrial Enlargement: Possible LAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Uncommon in partial; BVH in complete; RVH with Eisenmenger
*Particularities: Inferoposteriorly displaced AVN
==Patent ductus arteriosus==
Information about [[w:Patent_ductus_arteriosus|Patent ductus arteriosus on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, &uarr; IART/AF with age
*[[Conduction|PR interval]]: &uarr; PR 10% to 20%
*[[Heart axis|QRS axis]]: Normal
* QRS Configuration: Deep S V<sub>1</sub>, tall R V<sub>5</sub> and V<sub>6</sub>
* Atrial Enlargement: LAE with moderate PDA
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Uncommon
*Particularities: Often either clinically silent or Eisenmenger
==Pulmonary stenosis==
Information about [[w:Pulmonary_valve_stenosis|Pulmonary stenosis on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm
*[[Conduction|PR interval]]: Normal
*[[Heart axis|QRS axis]]: Normal if mild; RAD with moderate/severe
* QRS Configuration: Normal; or rSr&acute;; R&acute; increases with severity
* Atrial Enlargement: Possible RAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: RVH; severity correlates with R:S in V<sub>1</sub> and V<sub>6</sub>
*Particularities: Axis deviation correlates with RVP
==Aortic coarctation==
Information about [[w:Coarctation_of_the_aorta|Aortic coarctation on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm
*[[Conduction|PR interval]]: Normal
*[[Heart axis|QRS axis]]: Normal or LAD
* QRS Configuration: Normal
* Atrial Enlargement: Possible LAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: LVH, especially by voltage criteria
*Particularities: Persistent RVH rare beyond infancy
==Ebstein’s anomaly==
[[File:E000403.jpg|thumb|300px|ECG from a patient with Ebstein's anomaly showing huge P waves and low amplitude QRS waves. RBBB and T wave inversion are not present on this ECG.]]
[[File:DVA0559.jpg|thumb|300px|ECG from a patient with Ebstein's anomaly]]
Information about [[w:Ebstein's_anomaly|Ebstein's anomaly on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, possible EAR, SVT; AF/IART 40%
*[[Conduction|PR interval]]: 1° AVB common; short if WPW
*[[Heart axis|QRS axis]]: Normal or LAD
* QRS Configuration: Low-amplitude multiphasic atypical RBBB
* Atrial Enlargement: RAE with Himalayan P waves
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Diminutive RV
*Particularities: Accessory pathway common; Q II, III, aVF, and V<sub>1</sub>–V<sub>4</sub>
{{clr}}
==Surgically repaired TOF==
Information about [[w:Tetralogy_of_Fallot|Surgically repaired TOF on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm, PVCs; IART 10%; VT 12%
*[[Conduction|PR interval]]: Normal or mild &uarr;
*[[Heart axis|QRS axis]]: Normal or RAD; LAD 5% to 10%
* QRS Configuration: RBBB 90%
* Atrial Enlargement: Peaked P waves; RAE possible
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: RVH possible if RVOT obstruction or PHT
*Particularities: QRS duration&plusmn;QTd predictive of VT/SCD
==Congenitally corrected TGA==
Information about [[w:Levo-Transposition_of_the_great_arteries|Congenitally corrected TGA on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm
*[[Conduction|PR interval]]: 1° AVB &gt;50%; AVB 2%/year
*[[Heart axis|QRS axis]]: LAD
* QRS Configuration: Absence septal q; Q in III, aVF, and right precordium
* Atrial Enlargement: Not if no associated defects
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Not if no associated defects
*Particularities: Anterior AVN; positive T precordial; WPW with Ebstein’s
==Complete TGA/intra-atrial baffle==
*[[Rhythm]]: Sinus brady 60%; EAR; junctional; IART 25%
*[[Conduction|PR interval]]: Normal
*[[Heart axis|QRS axis]]: RAD
* QRS Configuration: Absence of q, small r, deep S in left precordium
* Atrial Enlargement: Possible RAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: RVH; diminutive LV
*Particularities: Possible AVB if VSD or TV surgery
==UVH with Fontan==
*[[Rhythm]]: Sinus brady 15%; EAR; junctional; IART &gt;50%
*[[Conduction|PR interval]]: Normal in TA; 1° AVB in DILV
*[[Heart axis|QRS axis]]: LAD in single RV, TA, single LV with noninverted outlet
* QRS Configuration: Variable; ↑R and S amplitudes in limb and precordial leads
* Atrial Enlargement: RAE in TA
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: RVH with single RV; possible LVH with single LV
*Particularities: Absent sinus node in LAI; AV block with L-loop or AVCD
==Dextrocardia / Situs inversus==
Information about [[w:Dextrocardia|Dextrocardia on Wikipedia (external link)]]
[[File:Puzzle_2007_12_426_fig1.jpg|thumb|300px|An example of dextrocardia]]
[[File:Situs_inversus.jpg|thumb|300px|Situs inversus]]
[[File:Situs_inversus_mirrored_lead_positioning.jpg|thumb|300px|Dextrocardia with mirrored lead positioning]]
*[[Rhythm]]: normal sinus rhythm, P-wave axis 105° to 165° with situs inversus
*[[Conduction|PR interval]]: Normal
*[[Heart axis|QRS axis]]: RAD
* QRS Configuration: Inverse depolarization and repolarization
* Atrial Enlargement: Not with situs inversus
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: LVH: tall R V<sub>1</sub>–V<sub>2</sub>; RVH: deep Q, small R V<sub>1</sub> and tall R right lateral
*Particularities: Situs solitus: normal P-wave axis and severe CHD
{{clr}}
==ALCAPA==
Information about [[w:Anomalous_Left_Coronary_Artery_From_the_Pulmonary_Artery|ALCAPA on Wikipedia (external link)]]
*[[Rhythm]]: normal sinus rhythm
*[[Conduction|PR interval]]: Normal
*[[Heart axis|QRS axis]]: Possible LAD
* QRS Configuration: Ant-lat Q waves; possible ant-sept Q waves
* Atrial Enlargement: Possible LAE
*[[Chamber_Hypertrophy_and_Enlargment|Ventricular hypertrophy]]: Selective hypertrophy of posterobasal LV
*Particularities: Possible ischemia
==References==
<biblio>
#khairy pmid=18056539
</biblio>

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