Abnormal Repolarization, Spot Diagnosis?
|Author(s)||A.A.M. Wilde, N.A. Blom|
|These Rhythm Puzzles have been published in the Netherlands Heart Journal and are reproduced here under the prevailing creative commons license with permission from the publisher, Bohn Stafleu Van Loghum.|
|The ECG can be enlarged twice by clicking on the image and it's first enlargement|
A boy with a birth weight of 3.030 g was born by caesarean section at 33 weeks of gestation because of bradycardia and severe foetal hydrops. Physical examination at birth showed a hydropic neonate with a heart rate of 70 beats/min. He had cutaneous syndactyly between the fourth and fifth fingers of the left hand. During the first week of life he suffered from polymorphic ventricular arrhythmias for which β- blocker treatment was started and an epicardial pacemaker (VVI) was implanted. An ECG a few weeks later is shown in the figure.
What is your diagnosis?